产品详情
This antibody detects endogenous levels of MCCB at Human/Mouse/Rat
免疫原详细信息
Synthesized peptide derived from human MCCB AA range: 204-254
相关试剂
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.108% sodium azide.
背景
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. [provided by RefSeq, Jul 2008],